Case report:noncompaction of the ventricular myocardium associated with polycystic kidney disease or hemivertebra
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Abstract: This report describesd two cases with the presentations of other anomalities.First case was a 26-years old man who had been admitted to our hospital because of chest tightness, dyspnea after the cold.There was high blood pressure of 160/110mmHg, with kidney failure of serum creatinine 234μmol/L.Ultrasound showed polycystic kidney, echocardiography revealed with unique features of prominent trabeculations of the myocardium and deep endocardial recesses.The trabeculation thickness was more than twice the thickness of the underlying. The diagnosis of isolated noncompaction of ventricular myocardium with polycystic kidney disease can be made. The second case was a 23-year old man who had been admitted to our hospital because of shortness of breath.His mother suffered from jaundice hepatitis during pregnancy.Eechocardiography revealed severely reduced left ventricular contraction, mild mitral regurgitation, thickened myocardium with prominent trabeculations and deep intertrabecular recesses.Lumbar magnetic resonance imaging (MRI) revealed congenital malformation of hemivertebra in L1L3.This was a case of NCM coupled with hemivertebra.
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[1] WEIFORD B C, SUBBARAO V D, MULHERN K M.Noncompaction of the ventricular myocardium[J].Circulation, 2007, 109:2965-2971.
[2] MOON J Y, CHUNG N, SEO H S, et al.Noncompaction of the ventricularmyocardium combined with polycystic kidney disease[J].Heart Vessels, 2006, 21:195-198.
[3] LUBRANO R, VERSACCI P G.Might there be an association between polycystic kidney disease and noncompaction of the ventricular myocardium?[J].Nephrol, Dial, Transplantat, 2009, 24:3884-3886.
[4] RAMINENI R, MERLA R, CHERNOBELSKY A.Noncompaction of ventricular myocardium associated with hypertrophic cardiomyopathy and polycystic kidney disease[J].Am J Med Sci, 2010, 339:383-386.
[5] 吴在德.外科学[M].6版.北京:人民卫生出版, 2005:826-827.
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