左心室心肌致密化不全心肌病的研究进展

李亮; 王梅; 张杨; 张国茹; 王亚玲; 李拥军

doi:10.13201/j.issn.1001-1439.2016.12.003

左心室心肌致密化不全心肌病的研究进展

- 河北医科大学第二医院东院区心内一科(石家庄, 050000)

详细信息

通讯作者: 李拥军,E-mail:liyongjun86632@sina.com

中图分类号: R542.2

收稿日期: 2016-05-12

修回日期: 2016-08-09

Research progress of left ventricular non-compaction cardiomyopathy

- Department of Cardiology, The Second Hospital of Hebei Medical University, Shijiazhuang, 050000, China

More Information

Corresponding author: LI Yongjun, E-mail: liyongjun86632@sina.com

Received Date: 12 May 2016

Revised Date: 09 August 2016

摘要

摘要: 左心室心肌致密化不全心肌病(LVNC)以突出的骨小梁、小梁隐窝以及左室心肌等表达紊乱为特点,主要表现为左室心尖处不正常的肌小梁形成,可合并左心室扩张,伴收缩、舒张功能不全,或合并各种形式的先天性心脏病,并会导致左心室、右心室或双心室的心力衰竭。本文就LVNC病的发病机制、流行病学、临床表现、诊断、治疗和预后进行综述。
- 致密化不全 /
- 心肌病 /
- 心力衰竭
Abstract: Left ventricular non-compaction cardiomyopathy (LVNC) is characterised by prominent trabeculae, intratrabecular recesses, and left ventricular myocardium abnormity, most frequently at the apex presenting with abnormal trabeculae.It can be associated with left ventricular dilation, systolic or diastolic dysfunction, or various forms of congenital heart disease. It can result in left heart failure, right heart failure or whole heart failure. The article focuses on the pathogenesis, epidemiology, clinical feature, diagnosis and prognosis of LVNC.
- non-compaction /
- cardiomyopathy /
- heart failure

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