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摘要: 嗜铬细胞瘤可诱发多种临床表现,其中应激性心肌病是其公认但罕见的临床表现。本文报道1例57岁女性患者,因突发气促就诊,临床表现类似急性冠状动脉综合征,病情进展快速且凶险,最后确诊为嗜铬细胞瘤诱发的应激性心肌病,行外科手术治疗,预后良好。Abstract: Pheochromocytoma can induce multiple clinical manifestations, among which stress-induced cardiomyopathy is a recognized but rare clinical manifestation of pheochromocytoma. This article reports a 57-year-old female patient who sought medical attention due to sudden shortness of breath. The clinical manifestations were similar to acute coronary syndrome, and the condition progressed rapidly and ominously. The final diagnosis was stress-induced cardiomyopathy induced by pheochromocytoma, and surgical treatment was performed with a good prognosis.
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Key words:
- pheochromocytoma /
- irritability cardiomyopathy /
- acute coronary syndrome
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表 1 血浆甲氧基肾上腺素类物质
Table 1. Plasma methoxy epinephrine substances
nmol/L 指标 结果 参考值 3-甲氧基酪胺 <0.08 <0.18 甲氧基肾上腺素 1.99 ≤0.50 甲氧基去甲肾上腺素 2.64 ≤0.90 注:若检测结果高于4倍参考范围上限,则强烈提示嗜铬细胞瘤或副神经节瘤。 -
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