致心律失常性右室心肌病的CMR研究进展

张凯璐; 曹玉坤; 史河水

doi:10.13201/j.issn.1001-1439.2025.02.003

致心律失常性右室心肌病的CMR研究进展

- 1.
  华中科技大学同济医学院附属协和医院放射科(武汉，430022)
- 2.
  湖北省分子影像重点实验室
基金项目:
湖北省自然科学基金面上项目(No：2024AFB669)

详细信息

通讯作者: 史河水，E-mail：heshuishi@hust.edu.cn

中图分类号: R542.2

收稿日期: 2024-04-18

刊出日期: 2025-02-13

Research progress on diagnosis of arrhythmogenic right ventricular cardiomyopathy in CMR

- 1.
  Department of Radiology, Tongji Medical College Affiliated Union Hospital, Huazhong University of Science and Technology, Wuhan, 430022, China
- 2.
  Key Laboratory of Molecular Imaging in Hubei

More Information

Corresponding author: SHI Heshui, E-mail: heshuishi@hust.edu.cn

Received Date: 18 April 2024

Publish Date: 13 February 2025

摘要

摘要: 致心律失常性右室心肌病(ARVC)是一种以纤维脂肪组织替代右室心肌、室性心律失常发生风险增加、具有较高心源性猝死发生风险的遗传性心肌病。心脏磁共振已成为评估ARVC患者心脏结构、功能和组织特征的主要影像学检查方法。本文将重点对心脏磁共振在ARVC中的诊断价值及最新研究进展进行综述。
- 致心律失常性右室心肌病 /
- 心脏磁共振 /
- 诊断
Abstract: Arrhythmogenic right ventricular cardiomyopathy(ARVC) is a hereditary cardiomyopathy characterized by the replacement of right ventricular myocardium with fibrous adipose tissue, increased occurrence of ventricular arrhythmias, and higher risk of sudden cardiac death. Cardiac magnetic resonance imaging has become the main imaging method for evaluating the cardiac structural, functional, and tissue characteristics of patients with ARVC. This review will focus on the diagnostic value and latest research progress of cardiac magnetic resonance imaging in ARVC.
- arrhythmogenic right ventricular cardiomyopathy /
- cardiac magnetic resonance imaging /
- diagnosis

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图 1 双心室心肌应变图

Figure 1. Strain map of biventricular myocardium

下载: 全尺寸图片幻灯片

图 2 典型ARVC病例的LGE图像

Figure 2. LGE images of typical ARVC case

下载: 全尺寸图片幻灯片

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