双室型致心律失常性右室心肌病1例

详细信息

收稿日期: 2024-01-12

刊出日期: 2025-02-13

Double ventricular arrhythmogenic right ventricular cardiomyopathy: one case report

- 1.
  Department of Ultrasound Medicine
- 2.
  Department of Cardiology, Xijing Hospital, Air Force Medical University, Xi'an, 710032, China

More Information

Received Date: 12 January 2024

Publish Date: 13 February 2025

摘要: 致心律失常性右室心肌病(arrhythmogenic right ventricular cardiomyopathy，ARVC)是一种遗传性心肌疾病，经典型主要影响右室，累及双室及左室者容易误诊和漏诊。本文报道双室型ARVC 1例，探讨其超声表现及其诊断标准、临床特征、发病机制和治疗，旨在提高对该病的认识及超声诊断率。
- 致心律失常性右室心肌病 /
- 心脏超声 /
- 诊断
Abstract: Arrhythmogenic right ventricular cardiomyopathy(ARVC) is a hereditary myocardial disease that mainly affects the right ventricle in the classic type. Patients with involvement of both ventricles and the left ventricle are prone to misdiagnosis and missed diagnosis. This article reports one case of biventricular ARVC, exploring its ultrasound manifestations, diagnostic criteria, clinical characteristics, pathogenesis, and treatment, in order to improve the ultrasound diagnosis rate of the disease.
- arrhythmogenic right ventricular cardiomyopathy /
- cardiac ultrasound /
- diagnosis

图 1 首次心电图

Figure 1. First ECG

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图 2 电复律后复查心电图

Figure 2. ECG after electrical cardioversion

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图 3 动态心电图

Figure 3. Dynamic ECG

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图 4 心脏二维超声

Figure 4. 2D echocardiography of the heart

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图 5 心脏声学造影显像

Figure 5. Echocardiographic contrast imaging of the heart

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图 6 电复律后复查心电图

Figure 6. ECG after electrical cardioversion

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图 7 CMR成像

Figure 7. CMR imaging

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