The diagnostic value and research advance of magnetic resonance imaging in connective tissue disease with cardiac injury
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摘要: 结缔组织疾病(CTD)是一大类因自身免疫机制失调所致的慢性炎症性免疫性疾病,可累及全身多系统、多器官,包括心脏。心脏各种结构在CTD多种病理生理机制共同作用下均可受累,并以亚临床损害多见。临床上,CTD患者一旦出现心力衰竭,往往提示预后不良。心脏磁共振是一种非侵入性、可重复性强的成像技术,在评价CTD患者心脏形态及功能、心肌水肿、微循环灌注及心肌纤维化方面提供了重要的临床价值。本文就心脏磁共振在CTD患者心脏损害中的诊断价值及研究进展予以综述。Abstract: Connective tissue disease(CTD) represents a heterogeneous group of chronic inflammatory autoimmune disorders derived from an auto-immunological deregulation and characterized by multisystem and multiorgan involvement, including the heart. Various cardiac structures can be affected by multiple pathophysiological mechanisms of CTD, and subclinical cardiac damage is more common. Once it becomes heart failure clinically, patients may present with a poor prognosis. Cardiac magnetic resonance(CMR) is a non-invasive and highly reproducible imaging technique that provides important clinical value in evaluating cardiac morphology and function, myocardial edema, microcirculation perfusion, and myocardial fibrosis in CTD patients. This review focuses on the diagnostic value and research progress of CMR in CTD patients with the cardiac injury.
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Key words:
- connective tissue disease /
- magnetic resonance imaging /
- diagnosis
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