隐藏于完全性右束支传导阻滞中的Brugada综合征

范子胤, 唐亮, 欧阳繁, 等. 隐藏于完全性右束支传导阻滞中的Brugada综合征[J]. 临床心血管病杂志, 2022, 38(6): 505-509. doi: 10.13201/j.issn.1001-1439.2022.06.015
引用本文: 范子胤, 唐亮, 欧阳繁, 等. 隐藏于完全性右束支传导阻滞中的Brugada综合征[J]. 临床心血管病杂志, 2022, 38(6): 505-509. doi: 10.13201/j.issn.1001-1439.2022.06.015
FAN Ziyin, TANG Liang, OUYANG Fan, et al. Brugada syndrome hidden in complete right bundle branch block[J]. J Clin Cardiol, 2022, 38(6): 505-509. doi: 10.13201/j.issn.1001-1439.2022.06.015
Citation: FAN Ziyin, TANG Liang, OUYANG Fan, et al. Brugada syndrome hidden in complete right bundle branch block[J]. J Clin Cardiol, 2022, 38(6): 505-509. doi: 10.13201/j.issn.1001-1439.2022.06.015

隐藏于完全性右束支传导阻滞中的Brugada综合征

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Brugada syndrome hidden in complete right bundle branch block

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  • 完全性右束支传导阻滞(CRBBB)在一般人群中比较常见,在健康人群中通常被认为是良性的。而Brugada综合征(BrS)是一种离子通道异常的遗传性心律失常性疾病,在没有结构性心脏病的情况下,BrS能增加心源性猝死的风险。然而,有研究证实CRBBB可覆盖BrS,从而使这类情况的诊断更具挑战性。本文对CRBBB掩盖BrS的相关研究进展作一综述,旨在为临床和科研工作者提供参考。
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  • 图 1  RBBB

    Figure 1.  RBBB

    图 2  CRBBB掩盖Brugada波,右室起搏使1型Brugada波显露

    Figure 2.  CRBBB masked Brugada wave, and right ventricular pacing exposed type 1 Brugada wave

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出版历程
收稿日期:  2021-08-09
刊出日期:  2022-06-13

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